Table 3.

General characteristics and morphologic analysis of sickle RBCs in four representative SCA patients. Symbols D, G, E and S indicate discoid-, granular-, elongated- and classic sickle-shaped RBCs, respectively.

conditionsamplesickling (%)fractionsickled cells (%)deformable cells (%)
DGESDGES
OxyOff-HUS-P-I0.0SS13.50.42.4
SS243.42.64.31.8
SS320.60.99.21.3
SS41.40.76.70.8
S-P-II0.0SS13.42.7
SS237.72.44.9
SS315.01.15.2
SS45.618.13.9
on-HUS-P-III0.0SS116.00.91.90.6
SS238.71.69.5
SS317.32.26.10.7
SS42.50.91.1
S-P-IV0.0SS12.50.6
SS228.81.9
SS355.63.8
SS43.12.50.60.6
short-term DeOxy (40 s)Off-HUS-P-I20.2SS12.60.53.0
SS24.438.22.45.71.6
SS35.81.814.71.67.80.4
SS42.55.10.61.3
S-P-II39.0SS12.81.71.6
SS236.84.73.5
SS312.50.35.40.52.7
SS40.612.55.97.21.3
On-HUS-P-III9.4SS118.01.00.4
SS23.138.47.50.8
SS34.415.86.3
SS41.40.51.60.8
S-P-IV3.1SS13.11.30.6
SS247.51.9
SS32.533.81.93.10.6
SS40.62.50.6
long-term DeOxy (4 min)Off-HUS-P-I59.5SS12.60.92.60.8
SS221.55.018.62.14.30.7
SS318.15.95.31.30.90.4
SS43.44.31.3
S-P-II80.4SS10.70.92.20.91.2
SS217.415.49.21.91.00.5
SS318.50.31.80.50.4
SS41.39.66.99.4
On-HUS-P-III34.4SS11.32.010.91.33.9
SS24.62.831.210.90.8
SS316.63.93.61.40.9
SS42.01.21.0
S-P-IV57.6SS12.50.6
SS27.57.515.6
SS331.34.423.7
SS45.01.9